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Pneumatosis Cystoides Intestinalis and Partial Abdominal Obstruction in a Patient with Polymyositis
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Ji Yeon Kim, Yong Hwan Kwon, Sang Jik Lee, Se Young Jang, Soo Young Park
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Intest Res 2011;9(3):234-237. Published online December 30, 2011
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DOI: https://doi.org/10.5217/ir.2011.9.3.234
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Abstract
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- Pneumatosis cystoides intestinalis (PCI) is a rare disease characterized by the presence of intramural gas-filled cysts in the gastrointestinal wall. This disease has been documented in patients with various medical conditions such as gastrointestinal disease, chronic obstructive lung disease, sepsis, and autoimmune disorders. A 49-year-old woman, who was undergoing immumosuppressant therapy due to polymyositis, developed PCI. She experienced a gradual onset of abdominal distension. A simple abdominal radiograph revealed small, round air shadows involving the small bowel, and abdominal computed tomography showed intraluminal air bubbles at the jejunal loop with free air in the peritoneum. Treatment with doxycycline effectively relieved the clinical symptoms and reduced the intramural gas. (Intest Res 2011;9:234-237)
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Citations
Citations to this article as recorded by 
- Pneumomediastinum, pneumatosis intestinalis and pneumoperitoneum in a patient with polymyositis: case-based review
Melis Dilbil, Funda Erbasan, Bengisu Aslan, Tahir Saygın Öğüt, Mine Nokay, Veli Yazısız, Mustafa Ender Terzioğlu Rheumatology International.2022; 43(4): 771. CrossRef - A Case of Pneumatosis Cystoides Intestinalis in a Patient with Dermatomyositis
Dong Jin Go, Jeong Seok Lee, Sang Hyun Joo, Jinyoung Moon, Jae Hyun Lee, Eun Young Lee Journal of Rheumatic Diseases.2015; 22(4): 238. CrossRef - Pneumatosis Cystoides Intestinalis with Pneumoperitoneum Complicating Systemic Sclerosis: A Case Report
Jae Uk Im, Eun Hye Kim, Hong Gil Jun, Ji Seon Oh, Seung Won Choi, Byeong Seong Kang Korean Journal of Medicine.2013; 84(6): 868. CrossRef - Recurrent pneumatosis intestinalis in a patient with dermatomyositis
Yousef Zarbalian, Erik C von Rosenvinge, William Twadell, Jamal Mikdashi BMJ Case Reports.2013; : bcr2013200308. CrossRef
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